Poland syndrome is a rare congenital disorder that primarily affects the skeletal and soft tissue structures of the chest, often accompanied by ipsilateral upper limb abnormalities. These include the absence or underdevelopment of ribs, pectoralis major and minor muscles, and the breast, as well as deformities such as syndactyly, brachydactyly, and even scoliosis. This condition most often manifests on the right side, though the left side may also be affected; bilateral involvement is rare. Poland syndrome can significantly alter an individual’s appearance and functionality.
Physical Manifestations of Poland Syndrome
In addition to the usual chest wall and upper limb deformities, Poland syndrome can cause respiratory symptoms, including chest tightness, palpitations, and shortness of breath, when chest wall integrity is significantly compromised. Furthermore, Poland syndrome may be accompanied by some specific diseases, such as Moebius syndrome and Klippel-Feil syndrome. In some cases, patients with Poland syndrome may also exhibit various tumors, especially breast cancer.
Treatments and Support at The Institute of Chest Wall Surgery (ICWS)
While there is no permanent cure for Poland syndrome, surgery remains the most effective option for improving both the function and appearance of the affected areas. The Institute of Chest Wall Surgery (ICWS) specializes in chest wall reconstructive surgery for Poland syndrome. ICWS offers personalized treatment plans to restore the chest wall’s form and function, ensuring a higher quality of life for individuals with this condition.
Conclusion
Through advanced surgical techniques, The Institute of Chest Wall Surgery (ICWS) provides effective solutions for individuals living with Poland Syndrome, helping them lead healthier and more fulfilling lives.
